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Cystic Fibrosis in Children and Adults: The Leeds method of management is a regularly updated resource for the treatment and management of cystic fibrosis. |
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| Contents |
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| Section
A: General principles;genetics;screening; presentation and making the
diagnosis
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| The basic problem | ||
| The genetics of cystic fibrosis | ||
| Antenatal screening | ||
| Antenatal diagnosis |
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| Presentation | ||
| Screening newborn infants for cystic fibrosis | ||
| Extended family screening or cascade screening | ||
| Making the diagnosis of cystic fibrosis | ||
| Section B: Management of the chest | ||
| Physiotherapy | ||
| Bronchoscopy | ||
| Oxygen for children with cystic fibrosis | ||
| Oxygen for adults with cystic fibrosis |
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| Non invasive ventilation | ||
| Respiratory infection |
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| Eradication regimens for early or recurrent Pseudomonas aeruginosa infection | ||
| Burkholderia cepacia complex (Bcc) | ||
| Staphylococcus aureus and Methicillin resistant Staphylococcus aureus (MRSA) | ||
| New microbial challenges | ||
| Stenotrophomonas maltophilia | ||
| Achromobacter xylosoxidans | ||
| Non tuberculous mycobacteria | ||
| Fungal infections | ||
| Management of Respiratory infections | ||
| Viral infections | ||
| Antibiotics | ||
| Prophylactic use: Staphylococcus aureus | ||
| New cough and respiratory exacerbations | ||
| Respiratory exacerbation and intravenous antibiotics | ||
| Antibiotic treatment of multi-resistant organisms | ||
| Desensitisation | ||
| Home intravenous antibiotic therapy | ||
| Totally implantable venous access | ||
| Anti-inflammatory agents | ||
| Corticosteroids | ||
| Non steroidal anti-infllammatory drugs | ||
| Defensins and cathelicidins | ||
| Leukotriene receptor antagonist | ||
| Alpha 1 antitrypsin and secretory leukoprotease inhibitors | ||
| Macrolides | ||
| Nebulisers and compressors | ||
| Bronchodilators | ||
| Antibiotics | ||
| Taurolidine | ||
| rhDNase | ||
| Hypertonic saline | ||
| Section C: Gastrointestinal and nutritional problems | ||
| Nutritional requirements | ||
| Evaluation of growth | ||
| Feeding infants and toddlers | ||
| Managing feeding behaviour problems | ||
| Feeding of school children | ||
| From adolescence | ||
| Dietary supplements | ||
| Nasogastric and enterostomy feeding | ||
| Pancreatic enzymes | ||
| Leeds recommendations for pancreatic enzyme replacement therapy | ||
| Pancreatic enzyme replacement when fasting | ||
| Pancreatic enzyme replacement with enteral tube feeds | ||
| Pancreatic enzyme replacement in patients who cannot swallow | ||
| Persistent malabsoption | ||
| Persisting bowel symptoms despite optimal treatment | ||
| Constipation as the cause of recurrent abdominal pain | ||
| Distal intestinal obstruction syndrome | ||
| Vitamins | ||
| Essential fatty acids (EFAs) | ||
| Appetite stimulants | ||
| Anabolic agents | ||
| Section D: Non pulmonary cystic fibrosis disease | ||
| Diabetes mellitus | ||
| Liver disease | ||
| Screening for liver disease | ||
| Treatment of liver disease | ||
| Liver transplantation | ||
| Hepatocellular carcinoma | ||
| Renal disease | ||
| Lung transplantation | ||
| Psychosocial aspects of lung transplant | ||
| Fertility and pregnancy | ||
| Fertility in men with cystic fibrosis | ||
| Fertility in women with cystic fibrosis | ||
| Contraceptive advise | ||
| Assisted reproduction | ||
| Pregnancy | ||
| Breast feeding | ||
| Pregnancy after lung transplant | ||
| Low bone mineral density and arthritis in cystic fibrosis | ||
| Low bone mineral density | ||
| Joint pain and arthritis | ||
| Ear, nose and throat symptoms in cystic fibrosis | ||
| Social worker | ||
| Introduction | ||
| Agencies and charities | ||
| benefit information | ||
| Section E: Organisation of care | ||
| Terminal care | ||
| Travel and cystic fibrosis | ||
| Flight assessment and cystic fibrosis | ||
| Section F: The future | ||
| Gene therapy | Out
soon |
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| Drug modulation of cystic fibrosis transmembrane conductance regulator | ||
| Ion transport modulation | ||
| New | The history of cystic fibrosis | |
| Links to cystic fibrosis related sites | ||
http://www.cysticfibrosismedicine.com and http://www.cfmedicine.com
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